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You are here:Home » Antibodies » Antibodies-Fibrillin » Anti -Fibrillin 2 (Fibrillin-2, FBN2, Congenital Contractural Arachnodactyly, CCA, DA9)

Anti -Fibrillin 2 (Fibrillin-2, FBN2, Congenital Contractural Arachnodactyly, CCA, DA9)


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Clone Host Grade Applications
Monoclonal Mouse Affinity Purified E IP IH IC
Fibrillin-2 is a part of the Fibrillin family of glycoproteins, which are essential factors in the formation and maintenance of elastic fibers known as microfibrils within the extracellular matrix. Various researchers have suggested that Fibrillin-2 has a role in the mediation of microfibril assembly during early elastogenesis. Defects in Fibrillin-2 are causal to a rare disorder involving autosomal dominant connective tissue known as congenital contractual arachnodactyly (CCA), also known as Beals syndrome or distal arthrogryposis type 9 (DA9), and is similar to Marfan syndrome.
Catalog #F4195-11C
Suitable for use in ELISA, Immunohistochemistry, Immunoprecipitation and Immunocytochemistry.
Other applications not tested.
Recommended DilutionsImmunohistochemistry (Paraffin): 1:50
Optimal dilutions to be determined by the researcher.
Positive ControlLiver cancer and papillary serous carcinoma tissue
Storage and StabilityMay be stored at 4°C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20°C. Aliquots are stable for 12 months. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
Clone TypeMonoclonal
Clone No10H6
FormSupplied as a liquid in 0.1M Tris-Glycine, pH 7.4, 150mM sodium chloride, 0.05% sodium azide.
PurityPurified by Protein G affinity chromatography.
ImmunogenRecombinant protein corresponding to human Fibrillin-2.
SpecificityRecognizes human Fibrillin-2.
Important NoteThis product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications without the expressed written authorization of United States Biological.

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