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You are here:Home » Antibodies » Abs to Enzymes, Glycosidase » Anti -GLA, NT (Alpha-galactosidase A, Alpha-D-galactoside Galactohydrolase, Alpha-D-galactosidase A, Agalsidase, Melibiase)

Anti -GLA, NT (Alpha-galactosidase A, Alpha-D-galactoside Galactohydrolase,
Alpha-D-galactosidase A, Agalsidase, Melibiase)

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Specifications

Clone Host Grade Applications
Polyclonal Rabbit Purified E B IH IC FC IF
GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
Catalog #G2035-48
ApplicationsSuitable for use in ELISA, Flow Cytometry, Immunocytochemistry/Immunofluorescence, Immunohistochemistry and Western Blot. Other applications not tested.
Recommended DilutionELISA: 1:1,000
Western Blot: 1:1,000
Immuncytochemistry/Immunofluorescence: 1:10 -1:50
Immunohistochemistry (paraffin): 1:10 -1:50
Optimal dilutions to be determined by the researcher.
Storage and StabilityMay be stored at 4°C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20°C. Aliquots are stable for at least 12 months. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
Clone TypePolyclonal
IsotypeIgG
HostRabbit
SourceHuman
ConcentrationAs reported
FormSupplied as a liquid in PBS, 0.09% sodium azide.
PurityPurified by ammonium sulfate precipitation.
ImmunogenKLH-conjugated synthetic peptide mapping to a fragment of residues within aa 83 -112 in the N-terminal region of human GLA, UniPot Accession # P06280
SpecificityRecognizes human GLA.
Important NoteThis product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications without the expressed written authorization of United States Biological.
Alternate namesEC=3.2.1.22


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